Idiopathic Intracranial Hypertension (Pseudotumor Cerebri)
Typical Symptoms
Michael Wall, MD
Department of Ophthalmology and Visual Sciences
University of Iowa
Peer Review Status: Internally Peer Reviewed
Creation Date: 1991
Last Revision Date: 2001
The symptoms most commonly reported by IIH patients followed by their frequency are:
- headache (94%)
- transient visual obscurations or blurring
(68%)
- pulse synchronous tinnitus or "wooshing noise" in
the ear (58%)
- pain behind the eye (44%)
- double vision (38%)
- visual loss (30%)
- pain with eye movement (22%)
Headache Headache is present in nearly all
patients with IIH and is the usual symptom for which
patients seek medical attention. The headaches of the IIH
patient are usually severe and daily; they are are often
throbbing. They are different from previous headaches, may
awaken the patient and usually last hours. Nausea is common
and vomiting less so. The headache is often the worst head
pain ever experienced. Although uncommon, the presence of
pain behind the eyeball that is worsened movements of the
eyes can occur.
Transient visual obscurations Visual obscurations
are episodes of transient blurred vision that usually last
less than 30 seconds and are followed by full recovery of
vision. Visual obscurations occur in about 3/4 of IIH
patients. The attacks may be involve one or both eyes. They
are not correlated with the degree of intracranial
hypertension or with the extent of optic nerve swelling.
Visual obscurations do not appear to be associated with poor
visual outcome.
Pulsatile intracranial noises Pulsatile
intracranial noises or pulse-synchronous tinnitus is common
in IIH. The sound is often unilateral. In patients with
intracranial hypertension, compression of the jugular vein
on the side of sound abolishes it. The periodic compressions
were thought to convert the laminar blood flow to turbulent.
Visual loss The most serious problem patients have
is vision loss. (Figure 9, 10) About 5% of patients go blind
in at least one eye. These are usually patients who do not
return for follow-up evaluation.
Figure 9. At typical visual field defect present using
Goldmann perimetry in an IIH patient. Notice the large blind
spot (black filled area) and the lower left indentation (an
inferior nasal nerve fiber bundle defect).
Figure 10. A similar inferior nasal nerve fiber bundle
defect in an IIH patient found with automated perimeter
(Humphrey perimeter). These defects may resolve fully with
treatment.
Title Page
|
|
|